Figure 35

Distribution of forms of amyloidosis seen in patients at the Mayo Clinic in 1996. Of the 135 patients with amyloidosis, 83% had the primary form. Familial, secondary, and senile amyloidosis accounted for less than 10% of patients. Localized amyloid is limited to the involved organ and never becomes systemic. In localized amyloidosis, the fibrils consist of an immunoglobulin light chain; however, the patients do not have a monoclonal protein in their serum or urine. Most localized amyloidosis occurs in the respiratory tract, genitourinary tract, or skin.

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